Circular RNAs (circRNAs), as endogenous non-coding RNAs, are prevalent in the transcriptomes of eukaryotes and regulate various aspects of organisms' life activities, including transcriptional regulation, epigenetic modification, signal transduction, and chromatin modification. These regulatory functions are closely and indispensably linked to a wide range of diseases. In recent years, with circRNA research deepened gradually, circRNAs related to pulmonary hypertension have been increasingly identified, making them a new focus in the current study of pulmonary hypertension pathogenesis. This article presents an overview of the current research status of circRNAs in the field of pulmonary arterial hypertension, elucidating their functional roles and mechanisms underlying the disease.